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Inborn errors of type I IFN immunity in patients with life-threatening COVID-19 期刊论文
Science, 2020
作者:  Qian Zhang;  Paul Bastard;  Zhiyong Liu;  Jérémie Le Pen;  Marcela Moncada-Velez;  Jie Chen;  Masato Ogishi;  Ira K. D. Sabli;  Stephanie Hodeib;  Cecilia Korol;  Jérémie Rosain;  Kaya Bilguvar;  Junqiang Ye;  Alexandre Bolze;  Benedetta Bigio;  Rui Yang;  Andrés Augusto Arias;  Qinhua Zhou;  Yu Zhang;  Fanny Onodi;  Sarantis Korniotis;  Léa Karpf;  Quentin Philippot;  Marwa Chbihi;  Lucie Bonnet-Madin;  Karim Dorgham;  Nikaïa Smith;  William M. Schneider;  Brandon S. Razooky;  Hans-Heinrich Hoffmann;  Eleftherios Michailidis;  Leen Moens;  Ji Eun Han;  Lazaro Lorenzo;  Lucy Bizien;  Philip Meade;  Anna-Lena Neehus;  Aileen Camille Ugurbil;  Aurélien Corneau;  Gaspard Kerner;  Peng Zhang;  Franck Rapaport;  Yoann Seeleuthner;  Jeremy Manry;  Cecile Masson;  Yohann Schmitt;  Agatha Schlüter;  Tom Le Voyer;  Taushif Khan;  Juan Li;  Jacques Fellay;  Lucie Roussel;  Mohammad Shahrooei;  Mohammed F. Alosaimi;  Davood Mansouri;  Haya Al-Saud;  Fahd Al-Mulla;  Feras Almourfi;  Saleh Zaid Al-Muhsen;  Fahad Alsohime;  Saeed Al Turki;  Rana Hasanato;  Diederik van de Beek;  Andrea Biondi;  Laura Rachele Bettini;  Mariella D’Angio’;  Paolo Bonfanti;  Luisa Imberti;  Alessandra Sottini;  Simone Paghera;  Eugenia Quiros-Roldan;  Camillo Rossi;  Andrew J. Oler;  Miranda F. Tompkins;  Camille Alba;  Isabelle Vandernoot;  Jean-Christophe Goffard;  Guillaume Smits;  Isabelle Migeotte;  Filomeen Haerynck;  Pere Soler-Palacin;  Andrea Martin-Nalda;  Roger Colobran;  Pierre-Emmanuel Morange;  Sevgi Keles;  Fatma Çölkesen;  Tayfun Ozcelik;  Kadriye Kart Yasar;  Sevtap Senoglu;  Şemsi Nur Karabela;  Carlos Rodríguez-Gallego;  Giuseppe Novelli;  Sami Hraiech;  Yacine Tandjaoui-Lambiotte;  Xavier Duval;  Cédric Laouénan;  COVID-STORM Clinicians†;  COVID Clinicians†;  Imagine COVID Group†;  French COVID Cohort Study Group†;  CoV-Contact Cohort†;  Amsterdam UMC Covid-19 Biobank†;  COVID Human Genetic Effort†;  NIAID-USUHS/TAGC COVID Immunity Group†;  Andrew L. Snow;  Clifton L. Dalgard;  Joshua D. Milner;  Donald C. Vinh;  Trine H. Mogensen;  Nico Marr;  András N. Spaan;  Bertrand Boisson;  Stéphanie Boisson-Dupuis;  Jacinta Bustamante;  Anne Puel;  Michael J. Ciancanelli;  Isabelle Meyts;  Tom Maniatis;  Vassili Soumelis;  Ali Amara;  Michel Nussenzweig;  Adolfo García-Sastre;  Florian Krammer;  Aurora Pujol;  Darragh Duffy;  Richard P. Lifton;  Shen-Ying Zhang;  Guy Gorochov;  Vivien Béziat;  Emmanuelle Jouanguy;  Vanessa Sancho-Shimizu;  Charles M. Rice;  Laurent Abel;  Luigi D. Notarangelo;  Aurélie Cobat;  Helen C. Su;  Jean-Laurent Casanova
收藏  |  浏览/下载:21/0  |  提交时间:2020/10/26
Autoantibodies against type I IFNs in patients with life-threatening COVID-19 期刊论文
Science, 2020
作者:  Paul Bastard;  Lindsey B. Rosen;  Qian Zhang;  Eleftherios Michailidis;  Hans-Heinrich Hoffmann;  Yu Zhang;  Karim Dorgham;  Quentin Philippot;  Jérémie Rosain;  Vivien Béziat;  Jérémy Manry;  Elana Shaw;  Liis Haljasmägi;  Pärt Peterson;  Lazaro Lorenzo;  Lucy Bizien;  Sophie Trouillet-Assant;  Kerry Dobbs;  Adriana Almeida de Jesus;  Alexandre Belot;  Anne Kallaste;  Emilie Catherinot;  Yacine Tandjaoui-Lambiotte;  Jeremie Le Pen;  Gaspard Kerner;  Benedetta Bigio;  Yoann Seeleuthner;  Rui Yang;  Alexandre Bolze;  András N. Spaan;  Ottavia M. Delmonte;  Michael S. Abers;  Alessandro Aiuti;  Giorgio Casari;  Vito Lampasona;  Lorenzo Piemonti;  Fabio Ciceri;  Kaya Bilguvar;  Richard P. Lifton;  Marc Vasse;  David M. Smadja;  Mélanie Migaud;  Jérome Hadjadj;  Benjamin Terrier;  Darragh Duffy;  Lluis Quintana-Murci;  Diederik van de Beek;  Lucie Roussel;  Donald C. Vinh;  Stuart G. Tangye;  Filomeen Haerynck;  David Dalmau;  Javier Martinez-Picado;  Petter Brodin;  Michel C. Nussenzweig;  Stéphanie Boisson-Dupuis;  Carlos Rodríguez-Gallego;  Guillaume Vogt;  Trine H. Mogensen;  Andrew J. Oler;  Jingwen Gu;  Peter D. Burbelo;  Jeffrey I. Cohen;  Andrea Biondi;  Laura Rachele Bettini;  Mariella D'Angio;  Paolo Bonfanti;  Patrick Rossignol;  Julien Mayaux;  Frédéric Rieux-Laucat;  Eystein S. Husebye;  Francesca Fusco;  Matilde Valeria Ursini;  Luisa Imberti;  Alessandra Sottini;  Simone Paghera;  Eugenia Quiros-Roldan;  Camillo Rossi;  Riccardo Castagnoli;  Daniela Montagna;  Amelia Licari;  Gian Luigi Marseglia;  Xavier Duval;  Jade Ghosn;  HGID Lab§;  NIAID-USUHS Immune Response to COVID Group§;  COVID Clinicians§;  COVID-STORM Clinicians§;  Imagine COVID Group§;  French COVID Cohort Study Group§;  The Milieu Intérieur Consortium§;  CoV-Contact Cohort§;  Amsterdam UMC Covid-19 Biobank§;  COVID Human Genetic Effort§;  John S. Tsang;  Raphaela Goldbach-Mansky;  Kai Kisand;  Michail S. Lionakis;  Anne Puel;  Shen-Ying Zhang;  Steven M. Holland;  Guy Gorochov;  Emmanuelle Jouanguy;  Charles M. Rice;  Aurélie Cobat;  Luigi D. Notarangelo;  Laurent Abel;  Helen C. Su;  Jean-Laurent Casanova
收藏  |  浏览/下载:14/0  |  提交时间:2020/10/26
Chemical composition, structures, and light absorption of N-containingaromatic compounds emitted from burning wood and charcoal inhousehold cookstoves 期刊论文
Atmospheric Chemistry and Physics, 2020
作者:  Mingjie Xie, Zhenzhen Zhao, Amara L. Holder, Michael D. Hays, Xie Chen, Guofeng Shen, James J. Jetter, and Qin'geng Wang
收藏  |  浏览/下载:6/0  |  提交时间:2020/06/29
A lysosomal switch triggers proteostasis renewal in the immortal C. elegans germ lineage (vol 551, pg 629, 2017) 期刊论文
NATURE, 2020, 580 (7802) : E5-E5
作者:  Lu, Zhihao;  Zou, Jianling;  Li, Shuang;  Topper, Michael J.;  Tao, Yong;  Zhang, Hao;  Jiao, Xi;  Xie, Wenbing;  Kong, Xiangqian;  Vaz, Michelle;  Li, Huili;  Cai, Yi;  Xia, Limin;  Huang, Peng;  Rodgers, Kristen;  Lee, Beverly;  Riemer, Joanne B.;  Day, Chi-Ping;  Yen, Ray-Whay Chiu;  Cui, Ying;  Wang, Yujiao;  Wang, Yanni;  Zhang, Weiqiang;  Easwaran, Hariharan;  Hulbert, Alicia;  Kim, KiBem;  Juergens, Rosalyn A.;  Yang, Stephen C.;  Battafarano, Richard J.;  Bush, Errol L.;  Broderick, Stephen R.;  Cattaneo, Stephen M.;  Brahmer, Julie R.;  Rudin, Charles M.;  Wrangle, John;  Mei, Yuping;  Kim, Young J.;  Zhang, Bin;  Wang, Ken Kang-Hsin;  Forde, Patrick M.;  Margolick, Joseph B.;  Nelkin, Barry D.;  Zahnow, Cynthia A.;  Pardoll, Drew M.;  Housseau, Franck;  Baylin, Stephen B.;  Shen, Lin;  Brock, Malcolm V.
收藏  |  浏览/下载:26/0  |  提交时间:2020/07/03
Nightside condensation of iron in an ultrahot giant exoplanet 期刊论文
NATURE, 2020, 580 (7805) : 597-+
作者:  Lu, Zhihao;  Zou, Jianling;  Li, Shuang;  Topper, Michael J.;  Tao, Yong;  Zhang, Hao;  Jiao, Xi;  Xie, Wenbing;  Kong, Xiangqian;  Vaz, Michelle;  Li, Huili;  Cai, Yi;  Xia, Limin;  Huang, Peng;  Rodgers, Kristen;  Lee, Beverly;  Riemer, Joanne B.;  Day, Chi-Ping;  Yen, Ray-Whay Chiu;  Cui, Ying;  Wang, Yujiao;  Wang, Yanni;  Zhang, Weiqiang;  Easwaran, Hariharan;  Hulbert, Alicia;  Kim, KiBem;  Juergens, Rosalyn A.;  Yang, Stephen C.;  Battafarano, Richard J.;  Bush, Errol L.;  Broderick, Stephen R.;  Cattaneo, Stephen M.;  Brahmer, Julie R.;  Rudin, Charles M.;  Wrangle, John;  Mei, Yuping;  Kim, Young J.;  Zhang, Bin;  Wang, Ken Kang-Hsin;  Forde, Patrick M.;  Margolick, Joseph B.;  Nelkin, Barry D.;  Zahnow, Cynthia A.;  Pardoll, Drew M.;  Housseau, Franck;  Baylin, Stephen B.;  Shen, Lin;  Brock, Malcolm V.
收藏  |  浏览/下载:57/0  |  提交时间:2020/07/03

Ultrahot giant exoplanets receive thousands of times Earth'  s insolation(1,2). Their high-temperature atmospheres (greater than 2,000 kelvin) are ideal laboratories for studying extreme planetary climates and chemistry(3-5). Daysides are predicted to be cloud-free, dominated by atomic species(6) and much hotter than nightsides(5,7,8). Atoms are expected to recombine into molecules over the nightside(9), resulting in different day and night chemistries. Although metallic elements and a large temperature contrast have been observed(10-14), no chemical gradient has been measured across the surface of such an exoplanet. Different atmospheric chemistry between the day-to-night ('  evening'  ) and night-to-day ('  morning'  ) terminators could, however, be revealed as an asymmetric absorption signature during transit(4,7,15). Here we report the detection of an asymmetric atmospheric signature in the ultrahot exoplanet WASP-76b. We spectrally and temporally resolve this signature using a combination of high-dispersion spectroscopy with a large photon-collecting area. The absorption signal, attributed to neutral iron, is blueshifted by -11 +/- 0.7 kilometres per second on the trailing limb, which can be explained by a combination of planetary rotation and wind blowing from the hot dayside(16). In contrast, no signal arises from the nightside close to the morning terminator, showing that atomic iron is not absorbing starlight there. We conclude that iron must therefore condense during its journey across the nightside.


Absorption lines of iron in the dayside atmosphere of an ultrahot giant exoplanet disappear after travelling across the nightside, showing that the iron has condensed during its travel.


  
Heterozygous diploid and interspecies SCRaMbLEing 期刊论文
NATURE COMMUNICATIONS, 2018, 9
作者:  Shen, Michael J.;  Wu, Yi;  Yang, Kun;  Li, Yunxiang;  Xu, Hui;  Zhang, Haoran;  Li, Bing-Zhi;  Li, Xia;  Xiao, Wen-Hai;  Zhou, Xiao;  Mitchell, Leslie A.;  Bader, Joel S.;  Yuan, Yingjin;  Boeke, Jef D.
收藏  |  浏览/下载:8/0  |  提交时间:2019/11/27
Electron tomography reveals details of the internal microstructure of desalination membranes 期刊论文
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 2018, 115 (35) : 8694-8699
作者:  Culp, Tyler E.;  Shen, Yue-xiao;  Geitner, Michael;  Paul, Mou;  Roy, Abhishek;  Behr, Michael J.;  Rosenberg, Steve;  Gu, Junsi;  Kumar, Manish;  Gomez, Enrique D.
收藏  |  浏览/下载:6/0  |  提交时间:2019/11/27
reverse osmosis  polyamide  transmission electron microscopy  tomography  voids  
Late inception of a resiliently oxygenated upper ocean 期刊论文
SCIENCE, 2018, 361 (6398) : 174-177
作者:  Lu, Wanyi;  Ridgwell, Andy;  Thomas, Ellen;  Hardisty, Dalton S.;  Luo, Genming;  Algeo, Thomas J.;  Saltzman, Matthew R.;  Gill, Benjamin C.;  Shen, Yanan;  Ling, Hong-Fei;  Edwards, Cole T.;  Whalen, Michael T.;  Zhou, Xiaoli;  Gutchess, Kristina M.;  Jin, Li;  Rickaby, Rosalind E. M.;  Jenkyns, Hugh C.;  Lyons, Timothy W.;  Lenton, Timothy M.;  Kump, Lee R.;  Lu, Zunli
收藏  |  浏览/下载:13/0  |  提交时间:2019/11/27